TriangleFOR PATIENTS · SOURCE READING
Inherited Pheochromocytoma
Source: Pheochromocytoma and Paraganglioma Treatment (PDQ®)–Patient Version, National Cancer Institute.
Source updated: April 10, 2025 · Captured 2026-09-09.
Selected source text with whitespace normalised. This Triangle page is not an NCI PDQ summary. Independent clinical review is pending.
Context: Treatment of Pheochromocytoma and Paraganglioma
In patients with inherited pheochromocytoma linked to multiple endocrine neoplasia (MEN2) or von Hippel-Lindau (VHL) syndrome, tumors often form in both adrenal glands. The tumors are usually benign.
Treatment for inherited pheochromocytoma that forms in one adrenal gland is surgery to completely remove the gland.
Treatment for inherited pheochromocytoma that forms in both adrenal glands or later forms in the remaining adrenal gland may be surgery to remove the tumor and as little normal tissue in the adrenal cortex as possible.
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These surgeries may help patients avoid life-long hormone replacement therapy, acute adrenal insufficiency, and health problems due to the loss of hormones made by the adrenal gland.
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Preserved source evidence · Independent clinical review pending · Not medical advice