TriangleHEALTH PROFESSIONAL · SOURCE READING
Surgery
Source: Childhood Soft Tissue Sarcoma Treatment (PDQ®)–Health Professional Version, National Cancer Institute.
Source updated: April 21, 2025 · Captured 2026-09-09.
Selected source text with whitespace normalised. This Triangle page is not an NCI PDQ summary.
Context: Treatment of Vascular Tumors / Angiosarcoma / Treatment of angiosarcoma
Localized disease can be cured by aggressive surgery. Complete surgical excision appears to be crucial for the long-term survival of patients with angiosarcomas and lymphangiosarcomas, despite evidence of tumor shrinkage in some patients who were treated with local or systemic therapy.[22,26-28] Data on liver transplant for localized angiosarcomas are limited.[29][Level of evidence C1]
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Evidence (surgery):
A review of 222 patients (median age, 62 years; range, 15–90 years) reported the following:[28]
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A review of 222 patients (median age, 62 years; range, 15–90 years) reported the following:[28]
An overall disease-specific survival (DSS) rate of 38% at 5 years.
A review of 222 patients (median age, 62 years; range, 15–90 years) reported the following:[28]
The 5-year DSS rate was 44% in 138 patients with localized, resected tumors but only 16% in 43 patients with metastases at diagnosis.
One case report suggested that liver transplant may contribute to prolonged disease-free survival.[30][Level of evidence C2]
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Preserved source evidence · Not medical advice