TriangleHEALTH PROFESSIONAL · SOURCE READING
Prognosis
Source: Childhood Soft Tissue Sarcoma Treatment (PDQ®)–Health Professional Version, National Cancer Institute.
Source updated: April 21, 2025 · Captured 2026-09-09.
Selected source text with whitespace normalised. This Triangle page is not an NCI PDQ summary.
Context: Treatment of Tumors of Uncertain Differentiation / Desmoplastic Small Round Cell Tumor
The overall prognosis for patients with desmoplastic small round cell tumor remains extremely poor, with reported rates of death at 90%. Greater than 90% tumor resection either at presentation or after preoperative chemotherapy may be a favorable prognostic factor for OS.[111,112]; [113][Level of evidence C1] Response to neoadjuvant chemotherapy and complete resection (near 100%) is associated with improved outcome.[106,114]
Publication references
Read the original reference and check its publication notices.
Preserved source evidence · Not medical advice