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HEALTH PROFESSIONAL · SOURCE READING

Treatment of extrarenal (extracranial) rhabdoid tumor

Source: Childhood Soft Tissue Sarcoma Treatment (PDQ®)–Health Professional Version, National Cancer Institute.

Source updated: April 21, 2025 · Captured 2026-09-09.

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Context: Treatment of Tumors of Uncertain Differentiation / Rhabdoid Tumor NOS (Extrarenal)

Treatment options for extrarenal (extracranial) rhabdoid tumor include the following:[135-137][Level of evidence C1]

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Surgical removal when possible.

Chemotherapy as used for soft tissue sarcomas (but no single regimen is currently accepted as best).

Radiation therapy.

Responses to alisertib have been documented in four patients with CNS atypical teratoid/rhabdoid tumors.[138] For more information about CNS atypical teratoid/rhabdoid tumors, see Childhood Central Nervous System Atypical Teratoid/Rhabdoid Tumor Treatment.

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Preserved source evidence · Not medical advice