HEALTH PROFESSIONAL · SOURCE READING

Desmoid-Type Fibromatosis

Source: Childhood Soft Tissue Sarcoma Treatment (PDQ®)–Health Professional Version, National Cancer Institute.

Source updated: April 21, 2025 · Captured 2026-09-09.

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Context: Treatment of Fibroblastic and Myofibroblastic Tumors

Desmoid-type fibromatosis has previously been called desmoid tumor or aggressive fibromatosis.

Desmoid-type fibromatosis has an extremely low potential to metastasize. The tumors are locally infiltrating, and surgical control can be challenging because of difficulty obtaining margins of resection that contain the entire infiltrating tumor.

Desmoid-type fibromatosis has a high potential for local recurrence. These tumors also have a highly variable natural history, including well documented examples of spontaneous regression.[1,2]

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Genomic alterations →Treatment of desmoid-type fibromatosis →Treatment options under clinical evaluation →

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Preserved source evidence · Not medical advice