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← Childhood Soft Tissue Sarcoma

FOR PATIENTS · SOURCE READING

Perivascular epithelioid cell tumors (PEComas)

Source: Childhood Soft Tissue Sarcoma (PDQ®)–Patient Version, National Cancer Institute.

Source updated: May 9, 2025 · Captured 2026-09-09.

Selected source text with whitespace normalised. This Triangle page is not an NCI PDQ summary. Independent clinical review is pending.

Context: Treatment of childhood soft tissue sarcoma / Tumors of unknown cell origin (the place where the tumor first formed is not known)

Treatment of newly diagnosed perivascular epithelioid cell tumors may include:

Source links and citations

surgery to remove the tumor

observation, followed by surgery

targeted therapy (sirolimus), for tumors that have certain gene changes and cannot be removed by surgery

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Preserved source evidence · Independent clinical review pending · Not medical advice