TriangleHEALTH PROFESSIONAL · SOURCE READING
Treatment of extraskeletal myxoid chondrosarcoma
Source: Childhood Soft Tissue Sarcoma Treatment (PDQ®)–Health Professional Version, National Cancer Institute.
Source updated: April 21, 2025 · Captured 2026-09-09.
Selected source text with whitespace normalised. This Triangle page is not an NCI PDQ summary.
Context: Treatment of Tumors of Uncertain Differentiation / Extraskeletal Myxoid Chondrosarcoma
Treatment options for extraskeletal myxoid chondrosarcoma include the following:
Surgery.
Radiation therapy.
Aggressive local control and resection of metastases led to OS rates of 87% at 5 years and 63% at 10 years. Tumors were relatively resistant to radiation therapy.[97] The therapeutic benefit of chemotherapy has not been established.
Source links and citations
There may be potential genetic targets for small molecules, but these need to be studied as part of a clinical trial. In an adult study, six of ten patients who received sunitinib achieved partial responses.[100]
Source links and citations
Publication references
Read the original reference and check its publication notices.
Preserved source evidence · Not medical advice